Fantini Jacopo, Sartori Arianna, Granato Antonio, Manganotti Paolo
Department of Medical, Surgical and Health Sciences, University of Trieste, Neurology Clinic, Headache Centre, Strada di Fiume 447, Cattinara Hospital, Trieste, Italy.
Department of Medical, Surgical and Health Sciences, University of Trieste, Neurology Clinic, Headache Centre, Strada di Fiume 447, Cattinara Hospital, Trieste, Italy.
Clin Neurol Neurosurg. 2017 Jul;158:12-14. doi: 10.1016/j.clineuro.2017.04.005. Epub 2017 Apr 10.
Cluster headache (CH) is a rare and severe syndrome characterized by the recurrence of unilateral pain attacks, of short duration (15-180min), and associated with ipsilateral cranial autonomic symptoms. Although, not formally included in the International Classification of Headache Disorders, hemiplegic cluster headache (HCH) is an even more rare subtype of CH in which typical attacks can be accompanied by visual, sensory, and/or aphasic migrainous auras that have a variable propensity to evolve in reversible hemi-motor symptoms. After its first description in 2002, only few cases of HCH have been reported and many open questions about its prevalence and pathophysiology still need to be addressed. We describe a case of a 41-year old male that fulfilled the ICHD criteria for episodic CH who experienced atypical attacks characterized by concomitant acute onset of sensory aura, aphasia and hemi-motor symptoms. We also provide a concise review of the available literature and discuss the prevalence and the possible pathogenesis of CH with hemiplegic features.
丛集性头痛（CH）是一种罕见且严重的综合征，其特征为单侧疼痛发作反复出现，持续时间短（15 - 180分钟），并伴有同侧颅自主神经症状。尽管偏瘫性丛集性头痛（HCH）未正式纳入《国际头痛疾病分类》，但它是CH中更为罕见的一种亚型，其典型发作可伴有视觉、感觉和/或失语性偏头痛先兆，这些先兆有不同的倾向发展为可逆性半侧运动症状。自2002年首次描述以来，仅报告了少数HCH病例，关于其患病率和病理生理学仍有许多未解决的问题。我们描述了一例41岁男性病例，该病例符合发作性CH的国际头痛疾病分类（ICHD）标准，经历了以感觉先兆、失语和半侧运动症状急性起病为特征的非典型发作。我们还对现有文献进行了简要综述，并讨论了伴有偏瘫特征的CH的患病率和可能的发病机制。
