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一例因子宫肌瘤行两次腹腔镜手术后发生的播散性腹膜平滑肌瘤病。

A case of disseminated peritoneal leiomyomatosis after two laparoscopic procedures due to uterine fibroids.

作者信息

Ciebiera Michał, Słabuszewska-Jóźwiak Aneta, Zaręba Kornelia, Jakiel Grzegorz

机构信息

First Department of Obstetrics and Gynecology, Center of Postgraduate Medical Education, Warsaw, Poland.

出版信息

Wideochir Inne Tech Maloinwazyjne. 2017;12(1):110-114. doi: 10.5114/wiitm.2017.66045. Epub 2017 Feb 15.

DOI:10.5114/wiitm.2017.66045
PMID:28446940
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5397541/
Abstract

Disseminated peritoneal leiomyomatosis (DPL) is a rare disorder characterized by the presence of multifocal nodules and tumors composed of proliferating smooth muscle tissue, spread throughout the peritoneum. Estrogens and progesterone are considered to be the main factors initiating the formation of disseminated leiomyomatosis. Disseminated peritoneal leiomyomatosis is often asymptomatic, and acyclic vaginal bleeding or pain in the lower abdomen is associated with leiomyomatous rebuilt uterus corpus. Disseminated peritoneal leiomyomatosis can have other ambiguous presentation. The difficulty in DPL diagnosis is that it is not always accompanied by scattered leiomyomas and can occur after menopause. Some cases of DPL are associated with surgical procedures on uterine fibroids, especially with the use of a morcellator. We present the case of a 39-year-old woman with DPL who underwent laparoscopic myomectomy and laparoscopic supracervical hysterectomy before the final diagnosis of DPL. After the complete surgical treatment performed in our center the patient is free of symptoms.

摘要

播散性腹膜平滑肌瘤病(DPL)是一种罕见的疾病,其特征是存在多灶性结节和由增殖的平滑肌组织构成的肿瘤,这些肿瘤遍布整个腹膜。雌激素和孕激素被认为是引发播散性平滑肌瘤病形成的主要因素。播散性腹膜平滑肌瘤病通常无症状,非周期性阴道出血或下腹部疼痛与平滑肌瘤性子宫体重建有关。播散性腹膜平滑肌瘤病可能有其他不明确的表现。DPL诊断的困难在于它并不总是伴有散在的平滑肌瘤,且可发生在绝经后。一些DPL病例与子宫肌瘤手术有关,尤其是使用粉碎器的情况。我们报告一例39岁患有DPL的女性病例,该患者在DPL最终诊断之前接受了腹腔镜子宫肌瘤切除术和腹腔镜次全子宫切除术。在我们中心进行完全手术治疗后,患者症状消失。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/821f18b24cd8/WIITM-12-29507-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/716ba2a355b0/WIITM-12-29507-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/a1ae402875dd/WIITM-12-29507-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/1e4de4f2c712/WIITM-12-29507-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/d4ff1387b713/WIITM-12-29507-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/8cb82069499c/WIITM-12-29507-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/821f18b24cd8/WIITM-12-29507-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/716ba2a355b0/WIITM-12-29507-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/a1ae402875dd/WIITM-12-29507-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/1e4de4f2c712/WIITM-12-29507-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/d4ff1387b713/WIITM-12-29507-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/8cb82069499c/WIITM-12-29507-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fc7a/5397541/821f18b24cd8/WIITM-12-29507-g006.jpg

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Leiomyomatosis peritonealis disseminata: A case report and review of the literature.播散性腹膜平滑肌瘤病:一例报告并文献复习
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