Han Xueguang, Song Haibo, Zhou Li, Jiang Chunling
Department of Anesthesiology and Translational Neuroscience Center, West China Hospital, Sichuan University, Chengdu 610041, China.
J Thorac Dis. 2017 Mar;9(3):E215-E218. doi: 10.21037/jtd.2017.02.63.
Cardiac rhabdomyoma, a type of benign myocardial tumor, is regarded as the most common fetal cardiac tumor. Rhabdomyomas are usually found before birth or during the first year of life. It is widely accepted that rhabdomyomas are strongly associated with tuberous sclerosis, and tend to regress spontaneously without surgical excision. However, if the tumor has caused significant obstruction or refractory arrhythmias, the surgery should be advocated. Most of the surgeries for pediatric cardiac tumors are performed under cardiopulmonary bypass (CPB) with cardioplegia. Here, we present a case of successful resection of a right ventricular rhabdomyoma obstructing the right ventricular outflow tract (RVOT) and involving pulmonary valve annulus in an infant, performed under the guidance of transesophageal echocardiography (TEE) on a beating heart.
心脏横纹肌瘤是一种良性心肌肿瘤，被认为是最常见的胎儿心脏肿瘤。横纹肌瘤通常在出生前或出生后第一年被发现。人们普遍认为横纹肌瘤与结节性硬化症密切相关，并且往往无需手术切除即可自发消退。然而，如果肿瘤已导致严重梗阻或难治性心律失常，则应提倡手术治疗。大多数小儿心脏肿瘤手术是在体外循环（CPB）和心脏停搏的情况下进行的。在此，我们报告一例婴儿右心室横纹肌瘤成功切除的病例，该肿瘤阻塞右心室流出道（RVOT）并累及肺动脉瓣环，手术在经食管超声心动图（TEE）引导下在跳动的心脏上进行。
