• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

噬血细胞性淋巴组织细胞增生症与川崎病一例:并存还是重叠诊断?

A Case of Hemophagocytic Lymphohistiocytosis and Kawasaki Disease: Concurrent or Overlapping Diagnoses?

作者信息

Bechtel Allison S, Joyce Michael

机构信息

University of Florida College of Medicine Jacksonville.

Nemours Specialty Care, Jacksonville, FL.

出版信息

J Pediatr Hematol Oncol. 2018 Jan;40(1):e32-e33. doi: 10.1097/MPH.0000000000000837.

DOI:10.1097/MPH.0000000000000837
PMID:28452857
Abstract

Hemophagocytic lymphohistiocytosis (HLH) is not always suspected at the time of presentation. It is often mistaken for other diagnoses; complicated by the fact that it is often associated with an inciting event that has significant overlap. Kawasaki disease, along with other disorders, such as Ebstein Barr Virus infection, are conditions that may lead HLH. Our patient had a presentation that was consistent with Kawasaki disease on initial presentation, however subsequently met the diagnostic criteria of HLH. It provided an interesting discussion about diagnoses with clinical criteria and how the overlap can sometimes delay or complicate initial diagnosis.

摘要

噬血细胞性淋巴组织细胞增生症(HLH)在初诊时并不总是能被怀疑到。它常常被误诊为其他疾病;其复杂性在于它通常与有显著重叠的诱发事件相关。川崎病以及其他疾病,如EB病毒感染,都是可能导致HLH的病症。我们的患者在初次就诊时表现符合川崎病,但随后符合了HLH的诊断标准。这引发了关于依据临床标准进行诊断以及这种重叠有时如何会延迟或使初始诊断复杂化的有趣讨论。

相似文献

1
A Case of Hemophagocytic Lymphohistiocytosis and Kawasaki Disease: Concurrent or Overlapping Diagnoses?噬血细胞性淋巴组织细胞增生症与川崎病一例:并存还是重叠诊断?
J Pediatr Hematol Oncol. 2018 Jan;40(1):e32-e33. doi: 10.1097/MPH.0000000000000837.
2
Hemophagocytic lymphohistiocytosis and Kawasaki disease: combined manifestation and differential diagnosis.噬血细胞性淋巴组织细胞增生症与川崎病:联合表现及鉴别诊断
Pediatr Blood Cancer. 2009 Sep;53(3):493-5. doi: 10.1002/pbc.22098.
3
A child with Epstein-Barr Virus-associated hemophagocytic lymphohistiocytosis complicated by coronary artery lesion mimicking Kawasaki disease.一名患有爱泼斯坦-巴尔病毒相关噬血细胞性淋巴组织细胞增生症并伴有类似川崎病的冠状动脉病变的儿童。
J Pediatr Hematol Oncol. 2013 Oct;35(7):e317-9. doi: 10.1097/MPH.0b013e31828e5281.
4
Macrophage activation syndrome/Hemophagocytic Lymphohistiocytosis and Kawasaki disease.巨噬细胞活化综合征/噬血细胞性淋巴组织细胞增生症与川崎病
Pediatr Blood Cancer. 2010 Sep;55(3):592. doi: 10.1002/pbc.22630.
5
Hemophagocytic lymphohistiocytosis at initiation of kawasaki disease and their differential diagnosis.川崎病发病初期的噬血细胞性淋巴组织细胞增生症及其鉴别诊断。
Pediatr Hematol Oncol. 2010 Apr;27(3):244-9. doi: 10.3109/08880011003623642.
6
Forme Fruste of HLH (haemophagocytic lymphohistiocytosis): diagnostic and therapeutic challenges.噬血细胞性淋巴组织细胞增生症(HLH)的顿挫型:诊断与治疗挑战
BMJ Case Rep. 2015 Jan 29;2015:bcr2014206190. doi: 10.1136/bcr-2014-206190.
7
Neonatal Adenovirus Infection Complicated by Hemophagocytic Lymphohistiocytosis Syndrome.新生儿腺病毒感染合并噬血细胞性淋巴组织细胞增生症。
Pediatrics. 2018 Apr;141(Suppl 5):S475-S480. doi: 10.1542/peds.2017-2061.
8
Clinical characteristics of hemophagocytic lymphohistiocytosis related to Kawasaki disease.与川崎病相关的噬血细胞性淋巴组织细胞增生症的临床特征
Pediatr Hematol Oncol. 2011 Apr;28(3):230-6. doi: 10.3109/08880018.2010.526685.
9
[Hemophagocytic lymphohistiocytosis in a patient with Kawasaki disease].
Zhonghua Er Ke Za Zhi. 2010 Jul;48(7):543-4.
10
Kawasaki disease preceding haemophagocytic lymphohistiocytosis: challenges for developing world practitioners.川崎病并发噬血细胞性淋巴组织细胞增生症:对发展中国家从业者的挑战。
Pediatr Blood Cancer. 2010 Jul 1;54(7):1023-5. doi: 10.1002/pbc.22422.

引用本文的文献

1
Macrophage Activation Syndrome in Kawasaki Disease: Insights from a Systematic Literature Review on Diagnosis, Clinical Features, and Treatment.川崎病中的巨噬细胞活化综合征:关于诊断、临床特征及治疗的系统文献综述见解
Children (Basel). 2025 Mar 11;12(3):349. doi: 10.3390/children12030349.