Prada-Madrid Jose Rolando, Franco-Chaparro Lina Patricia, Garcia-Wenninger Miguel, Palomino-Consuegra Tatiana, Stanford Nora, Castañeda-Hernández Diego Alejandro
Department of Plastic and Reconstructive Surgery, Hospital de San José - Hospital Infantil Universitario de San José, FUCS, Bogotá, Colombia.
J Craniofac Surg. 2017 May;28(3):675-678. doi: 10.1097/SCS.0000000000003459.
The objective is to describe a new surgical procedure developed in the San Jose Pediatric University Hospital for the management of syndromic synostosis of the metopic suture in a patient clinically diagnosed with Saethre-Chotzen syndrome.
The diagnosis of Saethre-Chotzen syndrome, bilateral coronal sutures, and metopic suture synostoses was made through photographic, anthropometric, exophthalmometric, and computed tomography analysis. The keel-like frontal bone deformity was corrected following resection using a fusiform osteotomy, remodelling was obtained by milling the edges, and the bony fragments were repositioned and fixed on the posterior wall of the frontal bone. Additionally, a fronto-orbital advancement with a self-stabilizing bar was performed.
The 1-year postoperative results showed improvement in the position of the fronto-orbital bar, adequate cranial expansion, satisfactory correction of the upper facial third alteration, and correction of the keel-like deformity.
The surgical approach has not previously been described in the literature and offers an alternative management for syndromic craniosyntostosis of the metopic suture, avoiding skull irregularities.
目的是描述圣何塞儿科大学医院开发的一种新手术方法，用于治疗临床诊断为塞特勒-肖滕综合征患者的额缝综合征性颅骨融合。
通过摄影、人体测量、眼球突出测量和计算机断层扫描分析，诊断塞特勒-肖滕综合征、双侧冠状缝和额缝融合。采用梭形截骨术切除后矫正龙骨样额骨畸形，通过铣削边缘进行重塑，将骨碎片重新定位并固定在额骨后壁上。此外，还进行了带自稳定杆的额眶前移术。
术后1年结果显示额眶杆位置改善、颅骨充分扩张、上面部三分之一改变得到满意矫正以及龙骨样畸形得到矫正。
该手术方法此前未见文献报道，为额缝综合征性颅骨融合提供了一种替代治疗方法，可避免颅骨不规则。
