一名患有Greig头多指（趾）综合征的患者出现纤维性骨病变和多种牙齿异常。

The occurrence of a fibro-osseous lesion and multiple dental anomalies in a patient with the Greig cephalopolysyndactyly syndrome.

作者信息

Pliskin M E, Haber B, Kornbrot A, Madani F, Lally E T

机构信息

Department of Oral Medicine, University of Pennsylvania School of Dental Medicine, Philadelphia.

出版信息

Oral Surg Oral Med Oral Pathol. 1988 Oct;66(4):475-9. doi: 10.1016/0030-4220(88)90272-1.

DOI:10.1016/0030-4220(88)90272-1

PMID:2847100

Abstract

The Greig cephalopolysyndactyly syndrome is an uncommon dysmorphic syndrome characterized by preaxial and postaxial polysyndactyly and minor craniofacial anomalies. It has an autosomal dominant inheritance. A review of the literature has failed to show documentation of any dental or oral abnormalities. Therefore, we report on a patient with Greig syndrome who had a maxillary fibro-osseous lesion and multiple dental and oral abnormalities.

摘要

Greig头多指（趾）综合征是一种罕见的畸形综合征，其特征为轴前和轴后多指（趾）畸形以及轻微的颅面异常。它具有常染色体显性遗传。文献综述未能显示有任何牙齿或口腔异常的记录。因此，我们报告了一名患有Greig综合征的患者，该患者有上颌骨纤维性骨病变以及多种牙齿和口腔异常。