Tyczyński Paweł, Michałowska Ilona, Wolny Rafał, Dobrowolski Piotr, Łazarczyk Hubert, Rybicka Justyna, Hoffman Piotr, Witkowski Adam
Department of Interventional Cardiology and Angiology, Institute of Cardiology, Warsaw, Poland.
Department of Radiology, Institute of Cardiology, Warsaw, Poland.
Int J Cardiol. 2017 Aug 1;240:183-186. doi: 10.1016/j.ijcard.2017.04.052. Epub 2017 Apr 25.
Left aberrant subclavian artery (LASA), is a type of right aortic arch (RAA) branching, which takes-off distally to the right subclavian artery and usually crosses behind the esophagus to the left upper limb. Taking into account the rarity of RAA, LASA is much more rarely seen than the right aberrant subclavian artery (RASA) originating from the left aortic arch. However, RAA may be associated with much more frequent presence of LASA, than left aortic arch with RASA. Anatomical LASA characteristics were not described up to date.
Individual patient records filed in the electronic database from a single high-volume tertiary cardiac center were retrospectively screened for the presence of RAA in the consecutive patients who underwent chest computed tomography from 2008 to 2016.
14 patients with LASA were identified. Only 3 were free of coexisting intra- or extra-cardiac anomalies. The most common defect was tetralogy of Fallot (3 patients). One patient had five congenital defects. Kommerell's diverticulum (KD) was present in 9 patients. In all patients the LASA course was retrotracheal and retroesophageal. In all but one patients esophageal modelling or compression by KD or LASA was present.
Knowledge of Kommerell's diverticulum presence and morphology as well as the LASA course during preinterventional work-up of patients with congenital heart defects is critical, since it may have surgical implications during corrective procedures.
左迷走锁骨下动脉(LASA)是右主动脉弓(RAA)分支的一种类型,它起源于右锁骨下动脉远端,通常在食管后方穿过至左上肢。鉴于RAA较为罕见,LASA比起源于左主动脉弓的右迷走锁骨下动脉(RASA)更为少见。然而,RAA合并LASA的情况可能比左主动脉弓合并RASA更为常见。目前尚未有关于LASA解剖特征的描述。
回顾性筛查了一家大型三级心脏中心电子数据库中2008年至2016年期间接受胸部计算机断层扫描的连续患者的个体病历,以确定是否存在RAA。
共识别出14例LASA患者。只有3例无心脏内或心脏外合并畸形。最常见的缺陷是法洛四联症(3例)。1例患者有5种先天性缺陷。9例患者存在Kommerell憩室(KD)。所有患者的LASA走行均位于气管后方和食管后方。除1例患者外,其余患者均存在KD或LASA对食管的塑形或压迫。
在先天性心脏病患者的介入前评估中,了解Kommerell憩室的存在及其形态以及LASA的走行至关重要,因为这可能在矫正手术中具有手术意义。