[一名患有与帕陶氏综合征相关的唇裂患儿的麻醉]

[Anesthesia in a child operated for cleft lip associated with Patau's syndrome].

作者信息

Kamal Manoj, Varghese Don, Bhagde Jeet, Singariya Geeta, Simon Annie Miju, Singh Amar

机构信息

Dr. S.N. Medical College, Department of Anesthesia, Jodhpur, Rajasthan, Índia.

Jodhpur Dental College, Department of Oral and Maxillofacial Surgery, Jodhpur, Rajasthan, Índia.

出版信息

Braz J Anesthesiol. 2018 Mar-Apr;68(2):197-199. doi: 10.1016/j.bjan.2017.04.005. Epub 2017 May 16.

DOI:10.1016/j.bjan.2017.04.005

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9391730/

Abstract

Patients with Patau's syndrome (Trisomy 13) have multiple craniofacial, cardiac, neurological and renal anomalies with very less life expectancy. Among craniofacial anomalies cleft lip and palate are common. These craniofacial and cardiac anomalies present difficulties with anesthesia. We therefore describe the anesthetic management in the case of a Trisomy 13 child for operated for cleft lip at 10 months of age.

摘要

患有帕陶氏综合征（13三体综合征）的患者存在多种颅面、心脏、神经和肾脏异常，预期寿命很短。在颅面异常中，唇腭裂很常见。这些颅面和心脏异常给麻醉带来了困难。因此，我们描述了一名10个月大接受唇裂手术的13三体综合征患儿的麻醉管理情况。

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Better prognosis in newborns with trisomy 13 who received intensive treatments: a retrospective study of 16 patients.16 例接受强化治疗的 13 三体综合征新生儿的更好预后：一项回顾性研究。

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