Department of Paediatric Respiratory Medicine and Paediatric Cystic Fibrosis Centre, Children's Hospital for Wales, Cardiff, CF14 4XN, UK.
Paediatr Respir Rev. 2018 Mar;26:10-12. doi: 10.1016/j.prrv.2017.03.007. Epub 2017 Mar 14.
This is arguably the most exciting era in the treatment of Cystic Fibrosis (CF) with the emergence of potentially disease modifying therapies. The last year has seen fewer landmark papers, with the consolidation of existing knowledge and advances in the understanding of the patho-physiology and management of CF.
这可以说是囊性纤维化 (CF) 治疗中最令人兴奋的时代，因为出现了潜在的可改变疾病的治疗方法。去年发表的重要论文较少，主要是对现有知识的巩固以及对 CF 的病理生理学和治疗的理解的进展。
