Petersen Sven, Tobisch Alexander, Puhl Gero, Kötter Ina, Wollina Uwe
Department of General-, Visceral- and Vascular Surgery, Asklepios Hospital Altona, Hamburg, Germany.
Department of Rheumatology, Clinical Immunology and Nephrology, Asklepios Hospital Altona, Hamburg, Germany.
Reumatologia. 2017;55(2):100-103. doi: 10.5114/reum.2017.67606. Epub 2017 Apr 28.
Systemic sclerosis (SSc) is an autoimmune connective tissue disorder. Anorectal involvement might typically cause fecal incontinence and rarely rectal prolapse. Here we report three female patients, who were admitted with a mean history of 10 years suffering from SSc. All patients presented with the initial symptom of anal incontinence, in all cases this was associated with rectal intussusception or rectal prolapse. The three women faced prolapse recurrence, independent of the initial procedure. After surgical removal of the prolapse, the incontinence remained. In SSc rectal prolapse syndrome might occur at an earlier age, and a primary prolapse of the ventral aspect of the rectal wall seems to be typical for this disease. If patients with prior diagnosis of SSc appear with third degree of fecal incontinence, it is suspected to be associated with rectal prolapse. The prolapse recurrence rate after surgery in SSc patients is high.
系统性硬化症（SSc）是一种自身免疫性结缔组织疾病。肛门直肠受累通常可能导致大便失禁，很少引起直肠脱垂。在此，我们报告三名女性患者，她们平均有10年的系统性硬化症病史。所有患者均以肛门失禁为初始症状，在所有病例中，这均与直肠套叠或直肠脱垂有关。这三名女性均面临脱垂复发，与初始手术无关。在手术切除脱垂后，失禁仍然存在。在系统性硬化症中，直肠脱垂综合征可能在较早年龄出现，直肠壁腹侧的原发性脱垂似乎是该病的典型表现。如果先前诊断为系统性硬化症的患者出现三度大便失禁，则怀疑与直肠脱垂有关。系统性硬化症患者手术后的脱垂复发率很高。
