El-Said Howaida G, Pockett Charissa R, Moore John W
Rady Children's Hospital, San Diego, University of California, San Diego, California.
Center at which the work was performed: Rady Children's Hospital, San Diego, California.
Catheter Cardiovasc Interv. 2017 Nov 15;90(6):982-985. doi: 10.1002/ccd.27138. Epub 2017 Jun 1.
The phenomenon of coronary steal is well known in the setting of HLHS (Hypoplastic Left Heart Syndrome) early after the Classical Norwood Operation. We report a rare case of an infant with HLHS [Severe Aortic Stenosis (AS), Mitral Stenosis (MS) and small Left Ventricle (LV)], who developed aortic regurgitation and presumed coronary steal late after the Sano Modification of the Norwood Procedure. Coronary steal developed secondary to progressive aortic and mitral regurgitation and resulted in poor right ventricular function and severe tricuspid regurgitation. We describe a novel interventional approach for obliteration of the LV cavity by using hydrogel coils. LV obliteration eliminated the presumed steal and resulted in improvement in ventricular function, tricuspid regurgitation and clinical course.
在经典诺伍德手术后早期的左心发育不全综合征(HLHS)情况下,冠状动脉窃血现象是众所周知的。我们报告了一例罕见的HLHS婴儿病例[严重主动脉瓣狭窄(AS)、二尖瓣狭窄(MS)和小左心室(LV)],该婴儿在诺伍德手术的佐野改良术后晚期出现主动脉瓣反流并推测发生冠状动脉窃血。冠状动脉窃血继发于进行性主动脉瓣和二尖瓣反流,导致右心室功能不良和严重三尖瓣反流。我们描述了一种使用水凝胶线圈闭塞左心室腔的新型介入方法。左心室闭塞消除了推测的窃血现象,并导致心室功能、三尖瓣反流和临床病程得到改善。