Vargas Canas Alberto, Rivas Mario, Guerrero Torrealba Rodrigo, Francisca Fajre Caamano María
Unidad de Neurología Hospital Santiago Oriente "Dr. Luis Tisné", Santiago, Chile.
Investigador Internacional Universidad Autónoma del Caribe, Santiago, Chile.
Ann Neurosci. 2017 May;24(1):57-60. doi: 10.1159/000464424. Epub 2017 Apr 21.
The Marchiafava-Bignami disease, characterized by demyelination and necrosis of the corpus callosum, has typically been associated with chronic alcohol intake, and clinically has various symptoms and signs. However, several cases have been reported without alcohol association, and these - according to several publications - have some common points, such as preference for female, related to malnutrition, and radiological involvement of the splenium of the corpus callosum. We report a case of a patient with the characteristics described above and whose clinical manifestation was Athetosis. The authors associate this manifestation with the somatotopic distribution of the corpus callosum, and contribute to the etiologic diagnosis of Athetosis as a manifestation of the Marchiafava-Bignami disease, which has not been reported in the medical literature according to our review of the database.
马尔恰法瓦-比尼亚米病以胼胝体脱髓鞘和坏死为特征,通常与长期饮酒有关,临床上有各种症状和体征。然而,已有多例无饮酒关联的病例报道,根据一些出版物,这些病例有一些共同点,比如好发于女性、与营养不良有关以及胼胝体压部的影像学受累。我们报告一例具有上述特征且临床表现为手足徐动症的患者。作者将这种表现与胼胝体的躯体定位分布相关联,并有助于将手足徐动症作为马尔恰法瓦-比尼亚米病的一种表现进行病因诊断,根据我们对数据库的检索,医学文献中尚未有此报道。