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法洛四联症、左心室血栓、主动脉夹层:罕见关联。

Tetralogy of Fallot, left ventricular clot, aortic dissection: rare association.

作者信息

Jariwala Pankaj, Kale Satya Sridhar, Sepur Lakshmana, Padma Kumar Edla Arjun

机构信息

1 Department of Cardiology, Maxcure-Mediciti Hospitals, Hyderabad, Telangana, India.

2 Department of Cardiothoracic Surgery, Maxcure-Mediciti Hospitals, Hyderabad, Telangana, India.

出版信息

Asian Cardiovasc Thorac Ann. 2017 Sep-Oct;25(7-8):534-536. doi: 10.1177/0218492317717420. Epub 2017 Jun 16.

DOI:10.1177/0218492317717420
PMID:28622727
Abstract

Cases of uncorrected adult tetralogy of Fallot are rare and mostly manifest secondary to complications. A 30-year-old man presented with progressive breathlessness and severe chest discomfort. Echocardiography revealed tetralogy of Fallot with a left ventricular apical clot and DeBakey type I dissection of the aorta. The patient underwent successful surgical correction. The combination of preoperative complications in the setting of uncorrected tetralogy of Fallot, such as a left ventricular clot and DeBakey type I dissection of the aorta, is very rare.

摘要

未经矫正的成人法洛四联症病例罕见,大多继发于并发症。一名30岁男性出现进行性呼吸困难和严重胸痛。超声心动图显示法洛四联症合并左心室心尖部血栓及主动脉DeBakey I型夹层。该患者接受了成功的手术矫正。在未经矫正的法洛四联症情况下,术前出现左心室血栓和主动脉DeBakey I型夹层等并发症的组合非常罕见。

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Tetralogy of Fallot and Aortic Dissection: Implications in Management.法洛四联症与主动脉夹层:对治疗的影响
JACC Case Rep. 2022 May 18;4(10):581-586. doi: 10.1016/j.jaccas.2022.02.021.
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Is there any association between aortic root rotation angle and aortic dissection?
主动脉根部旋转角度与主动脉夹层之间是否存在关联?
Indian J Thorac Cardiovasc Surg. 2020 May;36(3):181-185. doi: 10.1007/s12055-019-00859-2. Epub 2019 Sep 6.