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颅缝早闭——识别、临床特征与治疗。

Craniosynostosis - Recognition, clinical characteristics, and treatment.

机构信息

Chair of Surgery, Medical Faculty, University of Ljubljana, Ljubljana, Slovenia.

出版信息

Bosn J Basic Med Sci. 2018 May 20;18(2):110-116. doi: 10.17305/bjbms.2017.2083.

Abstract

Craniosynostosis is a developmental craniofacial anomaly, resulting in impairment of brain development and abnormally shaped skull. The main cause of craniosynostosis is premature closure of one or more cranial sutures. It usually occurs as an isolated condition, but may also be associated with other malformations as part of complex syndromes. When left untreated, craniosynostosis can cause serious complications, such as developmental delay, facial abnormality, sensory, respiratory and neurological dysfunction, anomalies affecting the eye, and psychological disturbances. Thus, early diagnosis, expert surgical techniques, postoperative care, and adequate follow-up are of vital importance in treating craniosynostosis.

摘要

颅缝早闭是一种发育性颅面畸形,导致脑发育受损和颅骨形状异常。颅缝早闭的主要原因是一个或多个颅骨缝过早闭合。它通常作为一种孤立的情况发生,但也可能与其他畸形一起作为复杂综合征的一部分。如果不治疗,颅缝早闭会导致严重的并发症,如发育迟缓、面部畸形、感觉、呼吸和神经功能障碍、影响眼睛的异常以及心理障碍。因此,早期诊断、专家手术技术、术后护理和充分的随访对于治疗颅缝早闭至关重要。

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