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一名8岁青春期前女孩的大网膜囊性淋巴管瘤伪装成黏液性卵巢肿瘤:诊断性影像学检查和腹腔镜辅助切除术的结果

Large Omental Cystic Lymphangioma Masquerading as Mucinous Ovarian Neoplasia in an 8-Year-Old Premenarchal Girl: The Findings from Diagnostic Imaging and Laparoscopic-Assisted Excision.

作者信息

Takeda Akihiro, Ito Hiroaki, Nakamura Hiromi

机构信息

Department of Obstetrics and Gynecology, Gifu Prefectural Tajimi Hospital, Tajimi, Gifu, Japan.

Department of Surgery, Gifu Prefectural Tajimi Hospital, Tajimi, Gifu, Japan.

出版信息

J Pediatr Adolesc Gynecol. 2017 Dec;30(6):659-662. doi: 10.1016/j.jpag.2017.06.003. Epub 2017 Jun 16.

Abstract

BACKGROUND

Omental cystic lymphangioma is an extremely rare abdominal mass caused by congenital malformation.

CASE

An 8-year-old premenarchal girl reported abdominal pain. Diagnostic imaging revealed a large multicystic mass measuring 22 cm in diameter, which occupied the entire abdominal cavity with ascites. Emergency laparoscopy revealed a ruptured large cystic mass originating from the greater omentum; this was followed by successful laparoscopic-assisted excision. The pathological diagnosis was omental cystic lymphangioma.

SUMMARY AND CONCLUSION

The present findings show that omental cystic lymphangioma masquerading as mucinous ovarian neoplasia was a rare cause of acute abdominal events in a young girl. The present case shows that minimally invasive surgery can be a feasible option, which might achieve a favorable outcome in a young patient with an omental cystic lymphangioma.

摘要

背景

网膜囊性淋巴管瘤是一种由先天性畸形引起的极为罕见的腹部肿块。

病例

一名8岁青春期前女孩主诉腹痛。诊断性影像学检查显示一个直径达22厘米的巨大多囊性肿块,占据整个腹腔并伴有腹水。急诊腹腔镜检查发现一个源自大网膜的破裂巨大囊性肿块;随后成功进行了腹腔镜辅助切除术。病理诊断为网膜囊性淋巴管瘤。

总结与结论

目前的研究结果表明,伪装成黏液性卵巢肿瘤的网膜囊性淋巴管瘤是年轻女孩急性腹部事件的罕见病因。本病例表明,微创手术可能是一种可行的选择,对于患有网膜囊性淋巴管瘤的年轻患者可能会取得良好的治疗效果。

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