Kurup Harikrishnan K N, Baliulis Giedrius, Haw Marcus P, Vettukattil Joseph J
Congenital Heart Center, Helen DeVos Children's Hospital of Spectrum Health, Grand Rapids, Michigan.
Congenital Heart Center, Helen DeVos Children's Hospital of Spectrum Health, Grand Rapids, Michigan.
Ann Thorac Surg. 2017 Jul;104(1):e75-e77. doi: 10.1016/j.athoracsur.2016.06.046.
Tetralogy of Fallot with absent pulmonary valve syndrome (TOF/APV) is a rare congenital malformation. Although pulmonary artery (PA) anomalies have been observed in TOF, its association with disconnected PA is extremely rare. We report successful stenting of the disconnected left PA in a 3-year-old boy with TOF/APV followed by surgical reimplantation. The significance of this transcatheter intervention for guidance during surgery and the importance of visualizing a ductal stump on angiography as an indicator of disconnected PA are discussed.
法洛四联症合并肺动脉瓣缺如综合征（TOF/APV）是一种罕见的先天性畸形。尽管在法洛四联症中已观察到肺动脉（PA）异常，但其与离断性肺动脉的关联极为罕见。我们报告了一名3岁患TOF/APV男孩离断性左肺动脉成功置入支架，随后进行手术再植入的病例。讨论了这种经导管介入对手术指导的意义以及在血管造影时将导管残端作为离断性肺动脉指标进行可视化的重要性。
