Blioskas Sarantis, Sotiriou Sotiris, Rizou Katerina, Koletsa Triantafyllia, Karkos Petros, Kalogera-Fountzila Anna, Markou Konstantinos
1st Department of Otorhinolaryngology, Head and Neck Surgery, Aristotle University of Thessaloniki, AHEPA Hospital, 1 Stilponos Kyriakidi St., 54636 Thessaloniki, Greece.
Pathology Department, Faculty of Medicine, Aristotle University of Thessaloniki, Thessaloniki, Greece.
Case Rep Med. 2017;2017:8327215. doi: 10.1155/2017/8327215. Epub 2017 May 29.
Plexiform neurofibromas are benign tumors that tend to occur in patients suffering from neurofibromatosis type 1 (NF-1). This report addresses a rare case where the tumor affected the parotid gland, deriving almost exclusively from the peripheral portion of the facial nerve. A 6-year-old male was referred to us complaining about a gradually enlarging swelling over the right parotid area. Imaging localized the lesion to the superficial lobe of the parotid gland, suggesting a neurofibroma. Cosmetic disfigurement and a functional deficit led us to perform complete surgical resection. Meticulous surgical dissection as well as auriculotemporal nerve origin made complete extirpation possible with almost zero morbidity and ensured alleviation of both aesthetic impairment and pain. This is the first case of an intraparotid PN in a pediatric NF-1 patient, which originated from branches of the auriculotemporal nerve and particularly from fibers of the autonomic nervous system. Radical surgical excision was decided according to established decision-making algorithms.
丛状神经纤维瘤是一种良性肿瘤，多见于1型神经纤维瘤病（NF-1）患者。本报告介绍了一例罕见病例，肿瘤累及腮腺，几乎完全起源于面神经外周部分。一名6岁男性因右腮腺区逐渐增大的肿物前来就诊。影像学检查将病变定位在腮腺浅叶，提示为神经纤维瘤。出于美观和功能缺陷的考虑，我们对其进行了完整的手术切除。细致的手术解剖以及耳颞神经的起源使得完全切除肿瘤成为可能，且几乎没有并发症，确保了美观缺陷和疼痛的缓解。这是首例发生在小儿NF-1患者腮腺内的丛状神经纤维瘤病例，该肿瘤起源于耳颞神经分支，特别是自主神经系统的纤维。根据既定的决策算法决定进行根治性手术切除。
