Toujani Sonia, Ben Mansour Amani, Mjid Meriem, Hedhli Abir, Cherif Jouda, Ouahchy Yassine, Beji Majed
Department of Respiratory, Research Unit 12SP06, Faculty of Medicine of Tunis, El Manar Tunis University, Rabta hospital, Tunisia.
Tanaffos. 2017;16(1):76-79.
We report the case of a 40-year-old man with acute respiratory failure syndrome that later proved to be an initial manifestation of antisynthetase syndrome. The diagnosis of this rare combination of a connective tissue disease and an acute respiratory failure is difficult in a previously asymptomatic patient. Early diagnosis and immunosuppressive therapy started precociously prevented the disease progression and resulted in a good outcome.
我们报告了一例40岁男性患者，其最初表现为急性呼吸衰竭综合征，后来被证实是抗合成酶综合征的首发表现。对于一名既往无症状的患者，诊断这种结缔组织病与急性呼吸衰竭的罕见组合颇具难度。早期诊断并尽早开始免疫抑制治疗可防止疾病进展，并带来良好预后。
