在Fontan循环中，由蛋白丢失性肠病引起的淋巴管扩张导致的胃肠道出血。
Gastrointestinal haemorrhage due to lymphangiectasia caused by protein-losing enteropathy in the Fontan circulation.
作者信息
Gras Pauline, Gottrand Frédéric, Godart François
机构信息
1Department of Pediatrics,Division of Pediatric Cardiology, Faculty of Medicine,Regional University Hospital Center of Lille,Lille,France.
2Division of Hepatology, Gastroenterology and Nutrition, Faculty of Medicine,Jeanne de Flandre Children's Hospital,Regional University Hospital Center of Lille, Lille,France.
出版信息
Cardiol Young. 2017 Oct;27(8):1641-1643. doi: 10.1017/S1047951117000853. Epub 2017 Jun 27.
We report the case of a 14-year-old boy with severe protein-losing enteropathy after Fontan surgery that led to lymphangiectasia, which caused gastrointestinal haemorrhage and required invasive treatment to stop the bleeding. Through this case and a review of the literature on protein-losing enteropathy after Fontan surgery, we highlight a rare and serious presentation of the disease and the difficulties of diagnosis and management.
我们报告了一例14岁男孩的病例，该男孩在Fontan手术后出现严重的蛋白丢失性肠病，导致淋巴管扩张，进而引起胃肠道出血，需要进行侵入性治疗来止血。通过该病例以及对Fontan手术后蛋白丢失性肠病文献的回顾，我们强调了该疾病罕见且严重的表现形式以及诊断和管理的困难。
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