Sharma Mitakshara, Mallya Varuna, Khurana Nita, Kumar Praveen, Duggal Rajan
Senior Resident, Department of Pathology, Maulana Azad Medical College, New Delhi, India.
Assistant Professor, Department of Pathology, Maulana Azad Medical College, New Delhi, India.
J Clin Diagn Res. 2017 May;11(5):ED03-ED04. doi: 10.7860/JCDR/2017/25326.9767. Epub 2017 May 1.
Congenital Vascular Malformations (CVM) represents a group of vascular anomalies that are the result of defective development of the vascular system. Lymphatic malformation consists of dilated lymphatic vessels caused by occlusion of the lymphatic drainage system due to congenital malformations or acquired causes such as the effects of trauma, infection, or surgery. Lymphaticovenous Malformation (LVM) is composed of lymphatic and venous channels. The most common sites are the neck and axilla. We report two cases of a four and a half-year-old and a seven-year-old child who presented with complaints of swelling in arm and groin respectively. A provisional diagnosis was made on radiological investigations. Excision was done and the diagnosis was confirmed on histopathology and immunohistochemistry. The cases which were presented as LVMs are rare congenital tumours and require a high index of suspicion on part of pathologist and surgeon to reach a definitive diagnosis.
先天性血管畸形（CVM）是一组血管异常，是血管系统发育缺陷的结果。淋巴管畸形由先天性畸形或后天性原因（如创伤、感染或手术的影响）导致淋巴引流系统阻塞而引起的扩张淋巴管组成。淋巴静脉畸形（LVM）由淋巴管和静脉通道组成。最常见的部位是颈部和腋窝。我们报告了两例分别为4岁半和7岁的儿童病例，他们分别因手臂和腹股沟肿胀前来就诊。通过影像学检查做出了初步诊断。进行了切除手术，并通过组织病理学和免疫组织化学确诊。表现为LVM的病例是罕见的先天性肿瘤，需要病理学家和外科医生高度怀疑才能做出明确诊断。
