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巨大孤立性经颅罗萨伊-多夫曼病伴鼻及鼻旁组织弥漫性受累:病例报告及文献复习

Giant isolated transcranial Rosai-Dorfman disease with diffuse involvement of nasal and paranasal tissues: case report and literature review.

作者信息

Zhong Zhihong, Fu Wei, Sun Yuhao, Sun Qingfang, Bian Liuguan

机构信息

a Department of Neurosurgery , Ruijin Hospital, Shanghai Jiao Tong University, School of Medicine , Shanghai , China.

出版信息

Br J Neurosurg. 2019 Jun;33(3):299-301. doi: 10.1080/02688697.2017.1344614. Epub 2017 Jul 3.

Abstract

Rosai-Dorfman disease (RDD) is an uncommon systemic histioproliferative disease process characterized by sinus histiocytosis with massive lymphadenopathy, and isolated transcranial RDD (ITRDD) is extremely rare. We report a patient with giant ITRDD with diffuse involvement of nasal and paranasal tissues.

摘要

罗萨伊-多夫曼病(RDD)是一种罕见的系统性组织细胞增生性疾病,其特征为窦组织细胞增生伴巨大淋巴结病,而孤立性经颅RDD(ITRDD)极为罕见。我们报告一例患有巨大ITRDD且鼻腔和鼻窦组织弥漫受累的患者。

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