Sanders Felipe H, Edwards Bryan A, Fusco Matthew, Oskouian Rod J, Tubbs R Shane, Johnston James M
Seattle Science Foundation, Seattle, WA, USA.
Pediatric Neurosurgery, Children's of Alabama, Birmingham, AL, USA.
Childs Nerv Syst. 2017 Sep;33(9):1445-1449. doi: 10.1007/s00381-017-3507-x. Epub 2017 Jul 6.
Sinus pericranii is a rare vascular malformation that connects the intracranial dural sinuses to the extracranial venous drainage system and is caused by either trauma or congenital defects. Although the majority of these vascular structures are due to trauma, some are congenital.
Herein, we report a 5-month-old patient with a very large and fluctuating subcutaneous mass over the occiput and the diagnosis of Crouzon's syndrome. The child presented with a large midline mass that on imaging, connected to the underlying torcular and was diagnosed as a sinus pericranii. At long-term follow-up and without operative intervention, the sinus pericranii resolved. This uncommon relationship is reviewed.
Premature closure of posterior fossa sutures as part of Crouzon's syndrome can present with large sinus pericranii. Such subcutaneous swellings might resolve spontaneously.
颅骨膜窦是一种罕见的血管畸形，它将颅内硬脑膜窦与颅外静脉引流系统相连，由外伤或先天性缺陷引起。虽然这些血管结构大多是由外伤导致的，但也有一些是先天性的。
在此，我们报告一名5个月大的患者，枕部有一个非常大且大小波动的皮下肿块，并诊断为克鲁宗综合征。患儿出现一个位于中线的大肿块，影像学检查显示该肿块与下方的窦汇相连，诊断为颅骨膜窦。经过长期随访且未进行手术干预，颅骨膜窦自行消退。本文对这种不常见的关系进行了综述。
作为克鲁宗综合征一部分的后颅窝缝线过早闭合可表现为巨大的颅骨膜窦。这种皮下肿胀可能会自行消退。
