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心包内畸胎瘤的迟发性偶然诊断——一例报告

Late incidental diagnosis of intrapericardial teratoma - A case report.

作者信息

Moura Garcia Annelisa, Nery Dantas Junior Roberto, Kai Chi Chang, Rodrigues Parga José

机构信息

Unidade de Radiologia, Departamento de Imagem Cardiovascular, Hospital Sirio-Libanês, São Paulo, SP, Brasil.

Unidade de Radiologia, Departamento de Imagem Cardiovascular, Hospital Sirio-Libanês, São Paulo, SP, Brasil.

出版信息

Rev Port Cardiol. 2017 Jul-Aug;36(7-8):571.e1-571.e4. doi: 10.1016/j.repc.2016.09.015. Epub 2017 Jul 8.

DOI:10.1016/j.repc.2016.09.015
PMID:28694004
Abstract

We report a case of intrapericardial teratoma, which is a rare primary cardiac tumor usually found in newborns and infants. Cardiac teratomas can cause respiratory failure, large accumulations of pericardial fluid and cardiac compression leading to death in the intrauterine or neonatal period. The case described is rare because it is of a 16-year-old asymptomatic girl with an intrapericardial tumor as an incidental echocardiographic finding. Cardiac magnetic resonance imaging showed a complex pericardial cyst. Due to the potential for malignant evolution, she was referred for surgery to remove the tumor and a diagnosis of teratoma was confirmed by histopathology. Clinical follow-up had a good outcome.

摘要

我们报告一例心包内畸胎瘤,这是一种罕见的原发性心脏肿瘤,通常见于新生儿和婴儿。心脏畸胎瘤可导致呼吸衰竭、心包大量积液和心脏受压,从而在宫内或新生儿期导致死亡。所描述的病例很罕见,因为患者是一名16岁无症状女孩,心包内肿瘤是经超声心动图偶然发现的。心脏磁共振成像显示为一个复杂的心包囊肿。由于存在恶性演变的可能性,她被转诊接受手术切除肿瘤,组织病理学确诊为畸胎瘤。临床随访结果良好。

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Late incidental diagnosis of intrapericardial teratoma - A case report.心包内畸胎瘤的迟发性偶然诊断——一例报告
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