Yang David, McLaren Sally, Van Vliet Chris, deSousa Jean-Louis, Gajdatsy Adam
a Sir Charles Gairdner Hospital , Perth , Australia.
b Lions Eye Institute , Perth , Australia.
Orbit. 2017 Oct;36(5):356-358. doi: 10.1080/01676830.2017.1337181. Epub 2017 Jul 12.
Granular cell tumour is a rare soft tissue tumour that can occur in any part of the body, but seldom in ocular adnexa. It usually behaves in a benign fashion. We report a case of a 54-year-old man with a well-demarcated, solitary, slow-growing orbital tumour which lead to significant ocular symptoms. The case was a diagnostic and therapeutic challenge due to its location and difficulty in obtaining tissue for a histological diagnosis. Surgical biopsy attempts were made but they all failed to uncover the true identity of the lesion. A definitive diagnosis was revealed with complete surgical excision of the tumour, which was challenging due to its size and close association with rectus muscle. This case has highlighted that orbital granular cell tumour may result in significant ocular symptoms. Adequate exposure to the anatomical site is the key to obtaining diagnosis and complete excision of a lesion.
颗粒细胞瘤是一种罕见的软组织肿瘤，可发生于身体的任何部位，但很少发生于眼附属器。它通常表现为良性。我们报告一例54岁男性患者，患有边界清晰、孤立、生长缓慢的眼眶肿瘤，该肿瘤导致了明显的眼部症状。由于其位置以及获取组织进行组织学诊断的困难，该病例在诊断和治疗上具有挑战性。曾尝试进行手术活检，但均未能明确病变的真实性质。肿瘤完整切除后得出了明确诊断，由于肿瘤大小以及与直肌的紧密关联，完整切除颇具挑战性。该病例突出表明眼眶颗粒细胞瘤可能导致明显的眼部症状。充分暴露解剖部位是获得病变诊断及完整切除的关键。
