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一名患有免疫失调、多内分泌腺病、肠病、X连锁(IPEX)综合征的成人的苔藓样皮炎。

Lichenoid Dermatitis in an Adult with Immune Dysregulation, Polyendocrinopathy, Enteropathy, X-Linked (IPEX) Syndrome.

作者信息

Choi Young M, Wang Yen T, Geng Bob, Garcia-Lloret Maria, Smart Chandra N

机构信息

David Geffen School of Medicine at University of California Los Angeles (UCLA), Los Angeles, CA.

Division of Dermatology, David Geffen School of Medicine at UCLA, Los Angeles, CA;

出版信息

Skinmed. 2017 Jun 1;15(3):231-234. eCollection 2017.

PMID:28705291
Abstract

A 23-year-old man presented to our practice with erythroderma and an unusual retiform eruption, along with alopecia universalis and nail dystrophy. He had had no skin findings at birth, but since early infancy had had localized eczematous eruptions of his skin. At 10 years of age, he had developed a generalized eczematous flare requiring hospitalization, and another generalized episode occurred in October 2010. He was prescribed prednisone 60 mg daily, which initially provided an improvement, but tapering of the corticosteroid resulted in another generalized flare.

摘要

一名23岁男性前来我院就诊,患有红皮病和一种不寻常的网状皮疹,同时伴有全秃和甲营养不良。他出生时无皮肤病变,但自婴儿早期起皮肤就有局限性湿疹样皮疹。10岁时,他出现了一次全身性湿疹发作,需要住院治疗,2010年10月又发生了一次全身性发作。他每天服用60毫克泼尼松,最初病情有所改善,但糖皮质激素减量后又出现了一次全身性发作。

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