经病理证实的IgG4相关性腹膜后纤维化自发缓解
Pathologically Proven Spontaneous Remission of IgG4-related Retroperitoneal Fibrosis.
作者信息
Yamakawa Hideaki, Sekine Akimasa, Yamanaka Yumie, Sadoyama Shinko, Baba Tomohisa, Hagiwara Eri, Okudela Koji, Ogura Takashi
机构信息
Department of Respiratory Medicine, Kanagawa Cardiovascular and Respiratory Center, Japan.
Department of Respiratory Medicine, Tokyo Jikei University Hospital, Japan.
出版信息
Intern Med. 2017;56(14):1867-1871. doi: 10.2169/internalmedicine.56.7996. Epub 2017 Jul 15.
Some forms of idiopathic retroperitoneal fibrosis (RF) have recently been considered to be a part of the spectrum of immunoglobulin G4 (IgG4)-related disease. This case report is the first description of a spontaneous remission in a patient with pathologically proven IgG4-related RF. Although the pathogenesis and long-term disease behavior of IgG4-related RF remains unknown, we believe that an initial assessment consisting of only careful monitoring might be one important strategy, especially in asymptomatic IgG4-related RF patients without nephropathy, while carefully monitoring these patients for the risk of recurrence.
某些形式的特发性腹膜后纤维化（RF）最近被认为是免疫球蛋白G4（IgG4）相关疾病谱的一部分。本病例报告首次描述了一例经病理证实的IgG4相关RF患者的自发缓解情况。尽管IgG4相关RF的发病机制和疾病长期行为尚不清楚，但我们认为，仅由仔细监测组成的初始评估可能是一种重要策略，尤其是对于没有肾病的无症状IgG4相关RF患者，同时要仔细监测这些患者的复发风险。
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