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以腰痛为表现的特发性腹膜后纤维化

Idiopathic Retroperitoneal Fibrosis Presenting as Low Back Pain.

作者信息

Sharma Shorabh, Paniagua-Morales Julian A, Cordoba Giovanni Gerardo, Then Eric O, Sharma Sapna

机构信息

Internal Medicine, St. Barnabas Hospital Health System, Bronx, USA.

Internal Medicine, Mahatma Gandhi Mission Institute of Health Sciences, Navi Mumbai, USA.

出版信息

Cureus. 2019 Feb 14;11(2):e4075. doi: 10.7759/cureus.4075.

DOI:10.7759/cureus.4075
PMID:31019853
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6464980/
Abstract

Retroperitoneal fibrosis is a rare condition characterized by the presence of fibrous inflammatory tissue in the retroperitoneal structures, such as the infrarenal great vessels and ureters. We are reporting an atypical case of an alcoholic who presented with chronic back pain and abnormal liver function tests. Abdominal imaging revealed an incidental, ill-defined, abnormal soft tissue mass in the left pelvis and mild to moderate left hydroureteronephrosis. Interventional radiology (IR)-guided core biopsy reported cores of dense fibrous tissue with extensive lymphoplasmacytic infiltrates, consistent with idiopathic retroperitoneal fibrosis (IRF). The patient had a left ureteral stent placed and, subsequently, had robotic surgery for ureteral reimplantation.

摘要

腹膜后纤维化是一种罕见疾病,其特征是在腹膜后结构(如下腔静脉和输尿管)中存在纤维性炎症组织。我们报告了一例非典型病例,一名酗酒者出现慢性背痛和肝功能检查异常。腹部影像学检查发现左盆腔有一个偶然发现的、边界不清的异常软组织肿块,以及轻至中度左肾盂输尿管积水。介入放射学(IR)引导下的粗针活检报告显示为致密纤维组织核心,伴有广泛的淋巴浆细胞浸润,符合特发性腹膜后纤维化(IRF)。该患者置入了左输尿管支架,随后接受了输尿管再植机器人手术。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9ef9/6464980/73f9eb1d1e21/cureus-0011-00000004075-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9ef9/6464980/73f9eb1d1e21/cureus-0011-00000004075-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9ef9/6464980/73f9eb1d1e21/cureus-0011-00000004075-i01.jpg

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Pathologically Proven Spontaneous Remission of IgG4-related Retroperitoneal Fibrosis.经病理证实的IgG4相关性腹膜后纤维化自发缓解
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