Herbert Anna, Khan Waseem Asrar, Madi Salem
Respiratory Medicine, Royal Albert Edward Infirmary, Wigan, UK.
BMJ Case Rep. 2017 Jul 18;2017:bcr-2017-219892. doi: 10.1136/bcr-2017-219892.
A 45-year-old man with a raised body mass index presented with an acute history of right lower chest pain and increasing breathlessness. C reactive protein, D dimer and cardiac echocardiography were negative, with mild bibasal atelectasis the only positive reported finding from erect chest X-ray and CT pulmonary angiogram. He was discharged with antibiotics for a chest infection. He remained severely breathless and was referred to the sleep-related breathing disorders clinic. He described shoulder pain, daytime tiredness and sleeping upright due to a ââ'¬Ëœsuffocatingââ'¬â"¢ sensation. The video demonstrates the clinical findings. The CT topogram confirmed bilateral diaphragmatic paralysis. Spirometry demonstrated an 80% reduction in forced vital capacity in the supine position, when compared with erect. Consultation with a neurologist yielded the diagnosis of neuralgic amyotrophy, leading to bilateral diaphragmatic paralysis. The respiratory symptoms have been controlled with night-time non-invasive ventilation, allowing him to sleep supine.
一名体重指数升高的45岁男性,出现右下胸痛和呼吸急促加重的急性病史。C反应蛋白、D二聚体和心脏超声心动图检查均为阴性,直立胸部X线和CT肺血管造影仅报告有轻度双肺底肺不张这一阳性发现。他因胸部感染接受抗生素治疗后出院。他仍严重呼吸急促,被转诊至睡眠相关呼吸障碍诊所。他描述有肩部疼痛、日间疲倦,因“窒息”感而需直立睡眠。视频展示了临床检查结果。CT平扫证实双侧膈神经麻痹。肺功能测定显示,与直立位相比,仰卧位时用力肺活量降低了80%。咨询神经科医生后诊断为神经性肌萎缩,导致双侧膈神经麻痹。夜间无创通气已控制了呼吸症状,使他能够仰卧睡眠。