Greco Federico, Faiella Eliodoro, Santucci Domiziana, Lisi Delia De, Vullo Gianguido Lo, Zobel Bruno Beomonte, Grasso Rosario Francesco
Unit of Diagnostic Imaging, Università Campus Bio-Medico di Roma, Rome, Italy.
Medical Oncology Department, Università Campus Bio-Medico di Roma, Rome, Italy.
J Kidney Cancer VHL. 2017 Jul 20;4(3):1-9. doi: 10.15586/jkcvhl.2017.79. eCollection 2017.
Cystic nephroma is a rare, benign multicystic lesion of the kidney. This tumor occurs both in children and in adults. In children, it is highly prevalent in males; in adults, it is more frequent in women. The term "cystic nephroma" represents two apparently different entities: pediatric cystic nephroma, a benign form thought to originate from metanephric tissue, and adult cystic nephroma, considered as a lesion of mixed epithelial stromal tumor. The clinical presentation may be a palpable mass or nonspecific symptoms such as abdominal pain, hematuria, and urinary tract infections. In this review, we summarize the ultrasound imaging features of cystic nephroma and describe the characteristics of the most common renal cystic lesions and the differential diagnosis of cystic nephroma with other renal cystic lesions.
囊性肾瘤是一种罕见的肾脏良性多囊性病变。这种肿瘤在儿童和成人中均可发生。在儿童中,男性发病率较高;在成人中,女性更为常见。“囊性肾瘤”一词代表两种明显不同的实体:小儿囊性肾瘤,一种被认为起源于后肾组织的良性形式;以及成人囊性肾瘤,被视为混合性上皮间质瘤的一种病变。临床表现可能为可触及的肿块或非特异性症状,如腹痛、血尿和尿路感染。在本综述中,我们总结了囊性肾瘤的超声影像学特征,并描述了最常见的肾囊性病变的特点以及囊性肾瘤与其他肾囊性病变的鉴别诊断。