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严重主动脉瓣关闭不全并发高安动脉炎。

Severe aortic regurgitation complicating Takayasu's arteritis.

作者信息

Alali Wala M, Alahmari Saeed A, Alhebaishi Yahya S, Alrashidi Seham A

机构信息

Department of Internal Medicine, Prince Sultan Military Medical City, Riyadh, Kingdom of Saudi Arabia. E-mail:.

出版信息

Saudi Med J. 2017 Aug;38(8):863-867. doi: 10.15537/smj.2017.8.12473.

DOI:10.15537/smj.2017.8.12473
PMID:28762441
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5556305/
Abstract

We present an uncommon case of a 48-year-old female patient with symptomatic presentation of a severe aortic regurgitation with aneurysm of the ascending aorta and progressive dyspnea. Detailed investigation of laboratory tests and imaging identified Takayasu's arteritis (TA) as the underlying etiology. Computed tomography scan revealed complete occlusion of the right carotid artery as well as stenosis at the origins of left subclavian and vertebral arteries. In addition, cardiac magnetic resonance angiogram showed aneurysm at the proximal segment of right subclavian artery. Intervention with corticosteroids effectively diminished the need for immediate surgical intervention. Treating physicians should always consider differential diagnosis of TA in the presence of atypical clinical findings in all patients with cardiac problems especially when there is valve involvement.

摘要

我们报告了一例罕见病例,一名48岁女性患者,有严重主动脉瓣反流、升主动脉瘤及进行性呼吸困难的症状表现。实验室检查和影像学的详细调查确定大动脉炎(TA)为潜在病因。计算机断层扫描显示右侧颈动脉完全闭塞,以及左锁骨下动脉和椎动脉起始处狭窄。此外,心脏磁共振血管造影显示右侧锁骨下动脉近端段有动脉瘤。使用皮质类固醇进行干预有效地减少了立即进行手术干预的必要性。对于所有有心脏问题的患者,尤其是存在瓣膜受累的情况时,治疗医生在出现非典型临床发现时应始终考虑大动脉炎的鉴别诊断。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4896/5556305/f96c91517315/SaudiMedJ-38-863-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4896/5556305/675904e6d1e4/SaudiMedJ-38-863-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4896/5556305/f96c91517315/SaudiMedJ-38-863-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4896/5556305/675904e6d1e4/SaudiMedJ-38-863-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4896/5556305/f96c91517315/SaudiMedJ-38-863-g002.jpg

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Effects of immunosuppressive and biological agents on refractory Takayasu arteritis patients unresponsive to glucocorticoid treatment.免疫抑制剂和生物制剂对糖皮质激素治疗无效的难治性大动脉炎患者的影响。
J Cardiol. 2017 May;69(5):774-778. doi: 10.1016/j.jjcc.2016.07.009. Epub 2016 Aug 25.
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Surgery for aortic regurgitation and aortic root dilatation in Takayasu arteritis.大动脉炎中主动脉瓣关闭不全和主动脉根部扩张的手术治疗。
Asian Cardiovasc Thorac Ann. 2015 Oct;23(8):901-6. doi: 10.1177/0218492315591291. Epub 2015 Jun 18.
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Aortic regurgitation in Takayasu's arteritis.
QJM. 2015 May;108(5):421-2. doi: 10.1093/qjmed/hcu204. Epub 2014 Oct 5.
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Diagnostic and classification criteria of Takayasu arteritis.Takayasu 动脉炎的诊断和分类标准。
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Management of Takayasu arteritis: a systematic review.Takayasu 动脉炎的治疗:系统评价。
Rheumatology (Oxford). 2014 May;53(5):793-801. doi: 10.1093/rheumatology/ket320. Epub 2013 Oct 4.
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Repair of aortic regurgitation due to Takayasu arteritis.大动脉炎所致主动脉瓣关闭不全的修复
Heart Surg Forum. 2013 Feb 1;16(1):E24-6. doi: 10.1532/HSF98.20121059.
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Cardiovascular manifestations of Takayasu arteritis and their relationship to the disease activity: analysis of 204 Korean patients at a single center.大动脉炎的心血管表现及其与疾病活动的关系:单中心 204 例韩国患者的分析。
Int J Cardiol. 2012 Aug 9;159(1):14-20. doi: 10.1016/j.ijcard.2011.01.094. Epub 2011 Feb 26.
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Takayasu arteritis in France: a single-center retrospective study of 82 cases comparing white, North African, and black patients.法国的高安动脉炎:一项对82例患者的单中心回顾性研究,比较白人、北非人和黑人患者。
Medicine (Baltimore). 2010 Jan;89(1):1-17. doi: 10.1097/MD.0b013e3181cba0a3.
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