Devaraja K, Sagar Prem, Chirom Amit Singh
Department of Otorhinolaryngology, Kasturba Medical College, Manipal, Karnataka, India.
Department of Otorhinolaryngology, All India Institute of Medical Sciences, New Delhi, Delhi, India.
BMJ Case Rep. 2017 Aug 7;2017:bcr-2017-220567. doi: 10.1136/bcr-2017-220567.
Tracheobronchopathia osteochondroplastica is a rare airway disease of unknown aetiology. Due to overlapping symptomology and lack of awareness, the condition is often missed resulting in unnecessary medical or surgical treatment. A male patient presented with a long-standing history of hoarseness and had earlier received treatment for bronchial asthma and tuberculosis. On evaluation, he had typical submucosal calcified nodules distributed throughout the trachea sparing the posterior membranous part. Although the biopsy confirmed the diagnosis of tracheobronchopathia osteochondroplastica in our case, histopathological examination is not always needed to make this diagnosis. Our patient has been kept under conservative management and is having non-progression of disease at 1-year follow-up. After having reviewed the literature related to pathophysiology and management of tracheobronchopathia osteochondroplastica, we emphasise on the fact that the treating physicians' awareness about this condition is the key to its diagnosis and management.
骨化性气管支气管病是一种病因不明的罕见气道疾病。由于症状重叠且认识不足,该病常被漏诊,导致不必要的药物或手术治疗。一名男性患者有长期声音嘶哑病史,曾接受过支气管哮喘和肺结核治疗。经评估,他在整个气管有典型的黏膜下钙化结节,后膜部未受累。尽管活检证实了我们病例中的骨化性气管支气管病诊断,但并非总是需要组织病理学检查来做出此诊断。我们的患者一直采取保守治疗,在1年的随访中病情无进展。在回顾了与骨化性气管支气管病的病理生理学和治疗相关的文献后,我们强调治疗医生对这种疾病的认识是其诊断和治疗的关键。