Dellon Elisabeth, Goldfarb Samuel B, Hayes Don, Sawicki Gregory S, Wolfe Joanne, Boyer Debra
Department of Pediatrics, University of North Carolina School of Medicine, Chapel Hill, North Carolina.
Division of Pulmonary Medicine, Department of Pediatrics, The Children's Hospital of Philadelphia, Perelman School of Medicine, University of Pennsylvania, Philadelphia, Pennsylvania.
Pediatr Pulmonol. 2017 Nov;52(S48):S61-S68. doi: 10.1002/ppul.23748. Epub 2017 Aug 8.
Pediatric lung transplantation has advanced over the years, providing a potential life-prolonging therapy to patients with cystic fibrosis. Despite this, many challenges in lung transplantation remain and result in worse outcomes than other solid organ transplants. As CF lung disease progresses, children and their caregivers are often simultaneously preparing for lung transplantation and end of life. In this article, we will discuss the current barriers to success in pediatric CF lung transplantation as well as approaches to end of life care in this population.