Cuglievan Branko, Menegaz Brian A, Garces Sofia, Rytting Michael E
Department of Pediatric Oncology, University of Texas MD Anderson Cancer Center, Houston, Texas, USA.
Department of Sarcoma Medical Oncology, University of Texas MD Anderson Cancer Center, Houston, Texas, USA.
BMJ Case Rep. 2017 Aug 11;2017:bcr-2017-220891. doi: 10.1136/bcr-2017-220891.
In children with newly diagnosed acute myeloid leukaemia (AML), myeloid sarcomas (MS) of the central nervous system (CNS) are rare. Since MS involving the CNS are potentially curable, timely recognition is paramount. Establishing a diagnosis may be problematic as they can easily mimic primary CNS neoplasms. We report the case of a 5-year-old boy with AML with t(8;21)(q22;q22) rearrangement who presented with a massive intracranial MS and rapid clinical deterioration suggestive of a meningioma or a primitive neuroectodermal tumour. The peripheral smear showed blasts with Auer rods. Urgent chemotherapy was started for AML with presumptive CNS MS. The mass resolved with chemotherapy, and treatment was consolidated with radiotherapy. Although exceedingly rare, this case highlights the potential for MS to present similarly to a primary CNS tumour. MS should be part of the differential diagnosis as part of a CNS mass, particularly if the complete blood count is abnormal.
在新诊断的急性髓系白血病(AML)患儿中,中枢神经系统(CNS)的髓系肉瘤(MS)很罕见。由于累及中枢神经系统的MS有潜在治愈可能,及时识别至关重要。由于它们很容易模仿原发性中枢神经系统肿瘤,因此确立诊断可能存在问题。我们报告了一例5岁患有t(8;21)(q22;q22)重排的AML男孩,他出现了巨大的颅内MS,并伴有提示脑膜瘤或原始神经外胚层肿瘤的快速临床恶化。外周血涂片显示有Auer小体的原始细胞。针对疑似中枢神经系统MS的AML开始了紧急化疗。肿块通过化疗消退,并通过放疗巩固治疗。尽管极为罕见,但该病例突出了MS表现与原发性中枢神经系统肿瘤相似的可能性。MS应作为中枢神经系统肿块鉴别诊断的一部分,特别是如果全血细胞计数异常。