Azhar Muhammad J
Department of Pediatrics, Nizwa Hospital, Nizwa, Sultanate of Oman.
Oman Med J. 2010 Oct;25(4):e017. doi: 10.5001/omj.2010.97.
We present a case of extradural hemorrhage, a rare and unusual complication associated with Sickle Cell Disease, from Nizwa, Oman. A 12-year old male child with Sickle cell disease (SD) was admitted to hospital with backache and pain in both lower Limbs. Clinical examination revealed an average built child with mild pallor, mild tenderness in the lower back and both legs. Rest of the examination was unremarkable including the Central Nervous System. The next day, the patient developed generalized convulsion and became unconscious with shallow breathing. CT of the brain revealed large extradural hemorrhage with shift of mid line structure. After prompt neurosurgical and a hematologic intervention, the child survived and is making progress in rehabilitation. Primary hemorrhagic stroke is a known but uncommon complication of sickle cell disease in childhood, but extradural hemorrhage is an even more rare complication.
我们报告了一例来自阿曼尼兹瓦的硬膜外出血病例，这是一种与镰状细胞病相关的罕见且不寻常的并发症。一名患有镰状细胞病（SD）的12岁男童因背痛和双下肢疼痛入院。临床检查发现该患儿体型中等，有轻度苍白，下背部和双腿有轻度压痛。包括中枢神经系统在内的其余检查均无异常。第二天，患者出现全身抽搐，昏迷，呼吸浅促。脑部CT显示硬膜外大量出血，中线结构移位。经过及时的神经外科和血液学干预，患儿存活下来，目前正在康复中。原发性出血性中风是儿童镰状细胞病已知但不常见的并发症，而硬膜外出血是一种更为罕见的并发症。
