Chattopadhyay Probodh K, Nagori Shakil Ahmed, Menon Rahul P, Balasundaram T
Department of Oral and Maxillofacial Surgery, Army Dental Centre (Research and Referral), Delhi Cantt-10, New Delhi, India.
Oral Maxillofac Surg. 2017 Dec;21(4):467-469. doi: 10.1007/s10006-017-0647-9. Epub 2017 Aug 30.
Hemophilic pseudotumor is a rare complication occurring in patients with hemophilia, frequently seen in the femur, tibia, pelvic bones, iliac bones, or rarely in the maxillofacial region.
A 7-year-old male reported with a spontaneous extra-oral swelling that was managed with pre-operative transfusion of factor IX along with curettage of the lesion. Our report presents only the fourth case in literature wherein this tumor presented in a patient with hemophilia B.
Hemophilic pseudotumor is a rare entity in the maxillofacial region. High degree of suspicion is required for diagnosis, and close coordination between the medical and surgical teams aids in management.
血友病性假肿瘤是血友病患者中罕见的并发症，常见于股骨、胫骨、骨盆骨、髂骨，很少见于颌面区域。
一名7岁男性因自发的口外肿胀前来就诊，术前通过输注IX因子并刮除病变进行治疗。我们的报告是文献中第四例血友病B患者出现这种肿瘤的病例。
血友病性假肿瘤在颌面区域是一种罕见的疾病。诊断需要高度怀疑，医疗团队和外科团队之间的密切协作有助于治疗。
