Grech Nicole, Ellul Ernest, Spiteri Neville, Milic Miljan
Ann Ital Chir. 2017 Mar 29;6:S2239253X17026767.
Solitary Fibrous Tumours(SFT), previously known as haemangiopericytoma, are rarely encountered in surgery. They arise from mesenchyme tissue and can occur at several sites in the body - head and neck, extremities, thorax, abdomen and retroperitoneal space. In the thorax, where they arise from the pleura, and abdomen they may attain a large size before giving rise to symptoms. Most SFT behave in a benign manner. However a number of them recur locally or metastasize. Recurrences can occur several years after excision of the primary tumour. Complete surgical excision remains the primary modality of treatment. But, in sites where complete excision is not possible, other modalities have been tried with varying success. Here, we describe a SFT of the mesentery of the small intestine, an uncommon manifestation of the tumour, recurring after a period of 19 years in a 55 year old female, and presenting to the Emergency Department as an acute abdomen caused by acute intestinal obstruction. Surgical excision of the tumour was performed together with primary anastomosis of the small intestine.
Acute abdomen, Late recurrence, Mesentery, Solitary Fibrous tumour.
孤立性纤维瘤(SFT),以前称为血管外皮细胞瘤,在外科手术中很少见。它们起源于间充质组织,可发生于身体的多个部位——头颈部、四肢、胸部、腹部和腹膜后间隙。在胸部,它们起源于胸膜,在腹部,它们可能在出现症状之前长得很大。大多数SFT表现为良性。然而,其中一些会局部复发或转移。复发可能在原发肿瘤切除数年之后发生。完整的手术切除仍然是主要的治疗方式。但是,在无法进行完整切除的部位,已经尝试了其他治疗方式,效果各异。在此,我们描述一例小肠系膜的SFT,这是该肿瘤的一种罕见表现,一名55岁女性在19年后复发,并以急性肠梗阻导致的急腹症形式就诊于急诊科。对该肿瘤进行了手术切除,并同时对小肠进行了一期吻合。
急腹症;晚期复发;系膜;孤立性纤维瘤