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儿童超急性脱髓鞘性脑脊髓炎:一种罕见病症。

Hyper Acute Demyelinating Encephalomyelitis of Childhood: A Rare Entity.

作者信息

Kushwaha Suman, Gupta Ashutosh, Agarwal Neha, Chaturvedi Sujata, Jha Deepak

机构信息

Department of Neurology, Pathology, Neurosurgery, Institute of Human Behaviour and Allied Sciences, New Delhi, India.

出版信息

Ann Indian Acad Neurol. 2017 Jul-Sep;20(3):316-318. doi: 10.4103/aian.AIAN_52_17.

Abstract

A young child with catastrophic neurological illness diagnosed as a rare variant of acute demyelinating encephalomyelitis (ADEM). She succumbed to her illness despite of aggressive and appropriate management. Malignant demyelinating encephalomyelitis should be considered in children who are refractory to the treatment of ADEM.

摘要

一名患有灾难性神经系统疾病的幼儿被诊断为急性脱髓鞘性脑脊髓炎(ADEM)的罕见变体。尽管进行了积极且恰当的治疗,她仍因病去世。对于ADEM治疗无效的儿童,应考虑恶性脱髓鞘性脑脊髓炎。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1e31/5586132/c20da8f22490/AIAN-20-316-g001.jpg

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