Sadineni Raghu Teja, Kumar B Santh, Chander N B, Boppana Durga Mahita
Department of Radiology, Dr. Pinnamaneni Siddhartha Institute of Medical Sciences and Research Foundation, Vijayawada, Andhra Pradesh, India.
Department of Pediatrics, Rainbow Hospitals, Vijayawada, Andhra Pradesh, India.
Int J Appl Basic Med Res. 2017 Jul-Sep;7(3):213-215. doi: 10.4103/ijabmr.IJABMR_389_16.
Hypoplastic left heart syndrome (HLHS) represents a variety of cardiac malformations that may result from errors in the early stages of cardiac development. HLHS includes a wide spectrum of cardiac malformations including hypoplasia of the left ventricle, ascending aorta, hypoplasia, or atresia of the aortic and mitral valves. Over the recent years, the improved resolution of advanced equipment with awareness and increased performance of second-trimester ultrasound examinations for the assessment of fetal anomalies have helped in understanding the spectrum and have expanded our knowledge of HLHS. They are one of the causes which constitute for neonatal morbidity and mortality and hence the rapid need for prenatal evaluation with ultrasound to detect cardiac anomalies. Prenatal recognition of disease also allows families to prepare for a child with a life-threatening defect by consultation with the multidisciplinary team that will care for their newborn and discussing the short- and long-term prognosis.
左心发育不全综合征(HLHS)代表了多种心脏畸形,这些畸形可能是由于心脏发育早期阶段的差错所致。HLHS包括一系列广泛的心脏畸形,包括左心室发育不全、升主动脉发育不全、主动脉瓣和二尖瓣发育不全或闭锁。近年来,先进设备分辨率的提高,以及孕中期超声检查用于评估胎儿异常的意识和性能的提升,有助于了解HLHS的范围,并扩展了我们对HLHS的认识。它们是导致新生儿发病和死亡的原因之一,因此迫切需要通过超声进行产前评估以检测心脏异常。疾病的产前识别还使家庭能够通过与将照顾其新生儿的多学科团队进行咨询并讨论短期和长期预后,为患有危及生命缺陷的孩子做好准备。