Kara Ibrahim, Erkin Alper, Erkengel MHalil Ibrahim, Asil Kiyasettin
Department of Cardiovascular Surgery, Faculty of Medicine, Sakarya University, Sakarya, Turkey. Email:
Department of Cardiovascular Surgery, Faculty of Medicine, Sakarya University, Sakarya, Turkey.
Cardiovasc J Afr. 2017 Jul 23;28(4):e6-e8. doi: 10.5830/CVJA-2016-087.
Giant aortic aneurysm is defined as an aneurysm of the aorta of greater than 10 cm in diameter. This rare condition is associated with a high risk of morbidity and mortality and it may lead to fatal complications such as rupture and/or dissection if not managed with proper surgical planning and expertise. Other than atherosclerosis, the main causes of giant ascending aortic aneurysms include Marfan and Ehlers-Danhlos syndromes. Herein we report on a young male patient who had had an aortic valve replacement five years earlier due to a bicuspid aortic valve leading to aortic failure, accompanied by aortic coarctation. He had an aneurysmal expansion rate of 1.81 cm/year to reach a final aneurysmal diameter of 13.25 cm, which, to our knowledge, represents the largest size ever reported in the literature for such lesions, and in which the redo and aneurysmal wall were adjacent to the sternal margins.
巨大主动脉瘤被定义为直径大于10厘米的主动脉瘤。这种罕见病症与高发病率和死亡率风险相关，如果没有适当的手术规划和专业技术进行处理，可能会导致诸如破裂和/或夹层等致命并发症。除动脉粥样硬化外，巨大升主动脉瘤的主要病因包括马凡综合征和埃勒斯-当洛综合征。在此，我们报告一名年轻男性患者，他五年前因二叶式主动脉瓣导致主动脉功能衰竭并伴有主动脉缩窄而接受了主动脉瓣置换术。他的动脉瘤扩张速率为每年1.81厘米，最终动脉瘤直径达到13.25厘米，据我们所知，这是此类病变在文献中报道的最大尺寸，并且再次手术区域和动脉瘤壁紧邻胸骨边缘。
