节段性色素沉着障碍：一种罕见的皮肤色素沉着异常形式。
Segmental pigmentation disorder: A rare form of cutaneous dyspigmentation.
作者信息
Balighi Kamran, Kamyab Kambiz, Azizpour Arghavan, Amini Elahe, Fahim Shabnam
机构信息
Depatment of Dermatology, Razi Hospital, Tehran University of Medical Sciences, Tehran, Iran.
Razi Hospital, Tehran University of Medical Sciences, Tehran, Iran.
出版信息
Caspian J Intern Med. 2017 Summer;8(3):223-225. doi: 10.22088/cjim.8.3.223.
BACKGROUND
Segmental pigmentation disorder (SegPD) is a rare type of cutaneous dyspigmentation. This hereditary disorder, first described some 20 years ago, is characterized by hypo and hyperpigmented patches on the trunk, extremities and less likely on the face and neck. These lesions are considered as a type of checkerboard pattern.
CASE PRESENTATION
Herein, we present a 26-year-old male who presented with hyperpigmented patches on his trunk, neck and upper extremities. Considering the clinical and histopathological findings, the diagnosis of SegPD was confirmed.
CONCLUSION
SegPD is a somewhat neglected entity which should be considered in differential diagnosis of pigmentation disorders.
背景
节段性色素沉着障碍（SegPD）是一种罕见的皮肤色素沉着异常类型。这种遗传性疾病大约在20年前首次被描述，其特征是躯干、四肢出现色素减退和色素沉着斑，而面部和颈部出现的可能性较小。这些损害被认为是一种棋盘状图案。
病例报告
在此，我们报告一名26岁男性，其躯干、颈部和上肢出现色素沉着斑。综合临床和组织病理学检查结果，确诊为节段性色素沉着障碍。
结论
节段性色素沉着障碍是一个在色素沉着性疾病鉴别诊断中应予以考虑但在一定程度上被忽视的疾病。
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