Hollowoa Blake, Lamps Laura W, Mizell Jason S, English George W, Bridge Julia A, Ram Roopa, Gardner Jerad M
1 University of Arkansas for Medical Sciences, Little Rock, AR, USA.
2 University of Michigan, Ann Arbor, MI, USA.
Int J Surg Pathol. 2018 Apr;26(2):174-179. doi: 10.1177/1066896917731517. Epub 2017 Sep 26.
Dedifferentiated liposarcoma is typically a nonlipogenic high-grade sarcoma that arises from well-differentiated liposarcoma. It most commonly presents as a large mass in the retroperitoneum. Significant involvement of the gastrointestinal tract by dedifferentiated liposarcoma is uncommon. We present a unique case of dedifferentiated liposarcoma radiographically mimicking a primary colon mass with resulting intussusception; stranding of the adjacent adipose tissue was presumed to be a secondary reactive change. On histopathologic analysis of the hemicolectomy specimen, a high-grade sarcoma was seen growing through the colonic wall, and the majority of the surrounding pericolonic adipose tissue was actually composed of well-differentiated liposarcoma with characteristic fibrous bands rather than benign fat with reactive fibrosis. This case raises awareness that well-differentiated liposarcoma and dedifferentiated liposarcoma can rarely present as a primary intestinal mass mimicking colon cancer or other more common entities. When radiographic examination shows a perigastrointestinal or retroperitoneal fatty mass and/or stranding of the fat adjacent to a solid gastrointestinal mass, this unusual scenario should be considered in the radiologic differential diagnosis. Pathologists should keep dedifferentiated liposarcoma in the initial histologic differential diagnosis for any high-grade spindle cell tumor of the retroperitoneum or intra-abdominal visceral organs.
去分化脂肪肉瘤通常是一种起源于高分化脂肪肉瘤的非脂肪生成性高级别肉瘤。它最常表现为腹膜后的巨大肿块。去分化脂肪肉瘤显著累及胃肠道的情况并不常见。我们报告了一例独特的去分化脂肪肉瘤病例,其影像学表现酷似原发性结肠肿块并导致肠套叠;相邻脂肪组织的条索状改变被推测为继发性反应性改变。对半结肠切除标本进行组织病理学分析时,可见一个高级别肉瘤生长穿透结肠壁,且周围大部分结肠旁脂肪组织实际上由具有特征性纤维带的高分化脂肪肉瘤组成,而非伴有反应性纤维化的良性脂肪。该病例提醒人们,高分化脂肪肉瘤和去分化脂肪肉瘤极少会表现为酷似结肠癌或其他更常见病变的原发性肠道肿块。当影像学检查显示胃肠道周围或腹膜后脂肪性肿块和/或实性胃肠道肿块邻近脂肪的条索状改变时,在放射学鉴别诊断中应考虑这种不寻常的情况。对于腹膜后或腹腔内脏器的任何高级别梭形细胞瘤,病理学家在初始组织学鉴别诊断时应考虑到去分化脂肪肉瘤。