Bostanci Busra, Korkut Emre, Unlu Nımet
Department of Pediatric Dentistry Faculty of Dentistry Abant Izzet Baysal University Turkey.
Department of Pediatric Dentistry Faculty of Dentistry Konya Necmettin Erbakan University Turkey.
J Istanb Univ Fac Dent. 2017 Apr 3;51(2):61-67. doi: 10.17096/jiufd.78944. eCollection 2017.
Marfan syndrome is an autosomal dominant disorder of connective tissue primarily characterized with anomalies affecting the musculoskeletal system, the cardiovascular system and the eyes. It has been suggested that early diagnosis of the syndrome is important, because of the risk of infective endocarditis. A 7-year-old female was referred to our clinic, with a chief complaint of dental crowding in the anterior region of mandible. It was observed that the patient needed multiple treatments based on detailed clinical and radiographic examinations. The treatment was carried out with antibiotic prophylaxis an hour prior to her appointment considering her profound caries. The patient was advised to visit regularly for follow up and she was referred for orthodontic evaluation.
马凡综合征是一种常染色体显性结缔组织疾病,主要特征为影响肌肉骨骼系统、心血管系统和眼睛的异常。有人提出,由于存在感染性心内膜炎的风险,该综合征的早期诊断很重要。一名7岁女性因下颌前部牙齿拥挤的主诉被转诊至我们诊所。经详细的临床和影像学检查发现,该患者需要多种治疗。考虑到她严重的龋齿情况,在预约就诊前一小时进行了抗生素预防治疗。建议患者定期复诊,并转诊进行正畸评估。