Schmid R, Allescher H D, Schepp W, Hölscher A, Siewert R, Schusdziarra V, Classen M
Department of Internal Medicine II, Technical University of Munich.
Hepatogastroenterology. 1988 Feb;35(1):34-7.
A case of glucagonoma syndrome in a 58-year-old male patient who had the typical skin lesions associated with severe hypoaminoacidemia is described. The decrease in amino acids has been proposed to be causally related to the dermatosis. Furthermore, it has been shown previously that somatostatin rapidly improves skin lesions in glucagonoma patients. Therefore, plasma amino acid levels were determined before and during an infusion of somatostatin prior to surgical removal of the tumor in the tail of the pancreas. During somatostatin infusion in combination with total parenteral nutrition, 10 out of 22 amino acids were in the normal range. Thus it seems unlikely that normalization of amino acid levels is responsible for the rapid improvement in skin lesions in glucagonoma patients. On the other hand it cannot be excluded that partial normalization of amino acids contributed to the observed healing process. Nevertheless, somatostatin administered prior to surgery is a useful therapeutic regimen in these patients.
本文描述了一例58岁男性患者的胰高血糖素瘤综合征,该患者伴有典型皮肤病变及严重低氨基酸血症。氨基酸水平降低被认为与皮肤病存在因果关系。此外,先前研究表明,生长抑素可迅速改善胰高血糖素瘤患者的皮肤病变。因此,在手术切除胰腺尾部肿瘤之前,测定了患者在输注生长抑素前后的血浆氨基酸水平。在生长抑素输注联合全胃肠外营养期间,22种氨基酸中有10种处于正常范围。因此,氨基酸水平正常化似乎不太可能是胰高血糖素瘤患者皮肤病变迅速改善的原因。另一方面,不能排除氨基酸部分正常化对观察到的愈合过程有贡献。尽管如此,术前给予生长抑素对这些患者是一种有用的治疗方案。