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Oral Cholic Acid Is Efficacious and Well Tolerated in Patients With Bile Acid Synthesis and Zellweger Spectrum Disorders.

作者信息

Heubi James E, Bove Kevin E, Setchell Kenneth D R

机构信息

Divisions of Pediatric Gastroenterology, Hepatology and Nutrition.

Pathology and Laboratory Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio.

出版信息

J Pediatr Gastroenterol Nutr. 2018 Feb;66(2):e57-e59. doi: 10.1097/MPG.0000000000001764.

DOI:10.1097/MPG.0000000000001764
PMID:28968290
Abstract
摘要

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Oral Cholic Acid Is Efficacious and Well Tolerated in Patients With Bile Acid Synthesis and Zellweger Spectrum Disorders.口服胆酸对胆汁酸合成障碍和泽尔韦格谱系障碍患者有效且耐受性良好。
J Pediatr Gastroenterol Nutr. 2018 Feb;66(2):e57-e59. doi: 10.1097/MPG.0000000000001764.
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Oral Cholic Acid Is Efficacious and Well Tolerated in Patients With Bile Acid Synthesis and Zellweger Spectrum Disorders.口服胆酸对胆汁酸合成及泽尔韦格谱系障碍患者有效且耐受性良好。
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The clinical and biochemical effectiveness and safety of cholic acid treatment for bile acid synthesis defects: a systematic review.胆酸治疗胆汁酸合成缺陷的临床及生化有效性与安全性：一项系统评价
Orphanet J Rare Dis. 2024 Dec 19;19(1):466. doi: 10.1186/s13023-024-03449-7.
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Recent developments in diagnostics and treatment of neonatal cholestasis.新生儿胆汁淤积症的诊断和治疗新进展。
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