Bamotra Ravi Kant, Kesarwani Prem Chandra, Qayum Shazia
Senior Resident, Department of Ophthalmology, GMCH, Chandigarh, India.
Senior Resident, Department of Ophthalmology, AIIMS, Rishikesh, Uttrakhand, India.
J Clin Diagn Res. 2017 Aug;11(8):ND01-ND02. doi: 10.7860/JCDR/2017/25521.10369. Epub 2017 Aug 1.
Alport syndrome is an inherited disease characterized by progressive renal failure, hearing loss, and ocular abnormalities like anterior lenticonus, corneal opacities, cataract, central perimacular and peripheral coalescing fleck retinopathies, and temporal retinal thinning. Although anterior lenticonus is common in Alport syndrome, simultaneous anterior and posterior lenticonus is a rare presentation. We report a case of a 22-year-old female with simultaneous anterior and posterior lenticonus presentation in which ocular examination lead to the detection of Alport syndrome. The patient had sensorineural deafness as well as microscopic haematuria. Clear lens extraction was performed in both eyes to eliminate lenticular irregular astigmatism for visual rehabilitation.
奥尔波特综合征是一种遗传性疾病,其特征为进行性肾衰竭、听力丧失以及眼部异常,如前圆锥形晶状体、角膜混浊、白内障、黄斑中心及周边融合性斑点状视网膜病变和颞侧视网膜变薄。虽然前圆锥形晶状体在奥尔波特综合征中很常见,但同时出现前后圆锥形晶状体的情况却很罕见。我们报告了一例22岁女性同时出现前后圆锥形晶状体的病例,并通过眼部检查确诊为奥尔波特综合征。该患者伴有感音神经性耳聋以及镜下血尿。双眼均进行了透明晶状体摘除术,以消除晶状体不规则散光,促进视力恢复。