Elzein Chawki, Subramanian Sujata, Ilbawi Michel
1 Advocate Children's Heart Institute, Advocate Children's Hospital, Oak Lawn, IL, USA.
World J Pediatr Congenit Heart Surg. 2019 Jan;10(1):116-120. doi: 10.1177/2150135117704615. Epub 2017 Oct 3.
Ebstein's anomaly is a rare congenital cardiac malformation that may present in the neonatal period with life-threatening physiologic derangement, especially when it is associated with circular shunt. Urgent surgical intervention is critical for survival because of hemodynamic compromise. We review our experience with surgical management of neonates with Ebstein's anomaly associated with circular shunt and review the literature for similar reported cases. The underlying pathophysiology and different options of treatment are discussed.
埃布斯坦畸形是一种罕见的先天性心脏畸形，在新生儿期可能表现为危及生命的生理紊乱，尤其是当它与环状分流相关时。由于血流动力学受损，紧急手术干预对生存至关重要。我们回顾了我们对伴有环状分流的埃布斯坦畸形新生儿的手术治疗经验，并查阅了相关文献以寻找类似的报道病例。文中还讨论了其潜在的病理生理学和不同的治疗选择。
