Mittal Jayesh, Manikandan Ramanitharan, Dorairajan Lalgudi Narayanan, Toi Pampa Ch
Department of Urology, JIPMER, Puducherry, India.
Department of Pathology, JIPMER, Puducherry, India.
J Indian Assoc Pediatr Surg. 2017 Oct-Dec;22(4):242-244. doi: 10.4103/0971-9261.214454.
Malignant pheochromocytoma in children manifesting as local recurrence with multiple lymph nodal metastasis is a rare entity. We report a case of a 14-year-old child with recurrent sporadic malignant pheochromocytoma presenting 8 years after primary surgery with retroperitoneal lymphadenopathy. The child underwent excision of the tumor along with retroperitoneal lymphadenectomy. Histopathology confirmed pheochromocytoma with extensive lymph node metastasis. The patient has no signs of disease recurrence till date. This report supports the long-term follow-up and aggressive surgical approach to remove all foci of tumor in recurrent pheochromocytoma.
表现为局部复发并伴有多处淋巴结转移的儿童恶性嗜铬细胞瘤是一种罕见的疾病。我们报告一例14岁儿童复发性散发性恶性嗜铬细胞瘤病例，该患儿在初次手术后8年出现腹膜后淋巴结肿大。患儿接受了肿瘤切除及腹膜后淋巴结清扫术。组织病理学证实为嗜铬细胞瘤伴广泛淋巴结转移。该患者至今无疾病复发迹象。本报告支持对复发性嗜铬细胞瘤进行长期随访并采取积极的手术方法以切除所有肿瘤病灶。
