Gopalakrishnan Arun, Sasidharan Bijulal, Tharakan Jaganmohan, Valaparambil Ajitkumar
Department of Cardiology, 29354 Sree Chitra Tirunal Institute for Medical Sciences and Technology , Thiruvananthapuram, Kerala, India.
Asian Cardiovasc Thorac Ann. 2018 Jan;26(1):50-53. doi: 10.1177/0218492317736962. Epub 2017 Oct 8.
We describe an unusual case of partial atrioventricular septal defect with malalignment of the septum primum to the left atrium with respect to the ventricular septum, committing the tricuspid valve to both ventricles (double-outlet right atrium). Abnormal attachment of the septum primum to the lateral aspect of mitral annulus resulted in left atrial outflow obstruction. The patient underwent successful surgical correction.
我们描述了一例罕见的部分型房室间隔缺损病例,其原发隔相对于室间隔向左心房错位,导致三尖瓣连接两个心室(右心房双出口)。原发隔异常附着于二尖瓣环外侧导致左心房流出道梗阻。该患者接受了成功的手术矫正。