Miyawaki Mari, Oda Seitaro, Hirata Kenichiro, Yuki Hideaki, Utsunomiya Daisuke, Hayashi Hidetaka, Sakamoto Yasumiko, Okamoto Shinichiro, Fujii Kazuhiko, Yamashita Yasuyuki
Department of Diagnostic Radiology Faculty of Life Sciences Kumamoto University 1-1-1 Honjyo Chuo-ku, Kumamoto 860-8556 Japan.
Department of Respiratory Medicine Faculty of Life Sciences Kumamoto University 1-1-1 Honjyo Chuo-ku, Kumamoto 860-8556 Japan.
Clin Case Rep. 2017 Sep 11;5(10):1732-1733. doi: 10.1002/ccr3.1180. eCollection 2017 Oct.
Granulomatosis with polyangiitis (GPA) is characterized by necrotizing granulomatous inflammation usually involving the upper and lower respiratory tracts and necrotizing vasculitis predominantly affecting small-sized vessels. Although categorized as a small vessel vasculitis, GPA can cause periaortitis and pericarditis. Physicians should recognize all categories of vasculitis can affect any size arteries.
肉芽肿性多血管炎(GPA)的特征是坏死性肉芽肿性炎症,通常累及上、下呼吸道,以及主要影响小血管的坏死性血管炎。尽管GPA被归类为小血管血管炎,但它可导致主动脉周炎和心包炎。医生应认识到所有类型的血管炎都可能影响任何大小的动脉。