From the *Department of Thoracic and Cardiovascular Surgery and †Nuclear Medicine, Jeju National University Hospital, Jeju National University School of Medicine, Jeju, Korea.
Clin Nucl Med. 2017 Dec;42(12):976-977. doi: 10.1097/RLU.0000000000001875.
We report the case of a 19-year-old man who presented with a 12-year history of progressive fatigue, feeling hot, excessive sweating, and numbness in the left arm. He had undergone multimodal imaging and was diagnosed as having Klippel-Trénaunay-Weber syndrome (KTWS). This is a rare congenital disease, defined by combinations of nevus flammeus, venous and lymphatic malformation, and hypertrophy of the affected limbs. Lower extremities are affected mostly. Conventional modalities for evaluating KTWS are ultrasonography, CT, MRI, lymphoscintigraphy, and angiography. There are few reports on multimodal imaging of upper extremities of KTWS patients, and this is the first report of an infrared thermography in KTWS.
我们报告了一例 19 岁男性患者,他有 12 年的进行性疲劳、发热、过度出汗和左臂麻木病史。他曾接受过多种模式的影像学检查,被诊断为 Klippel-Trénaunay-Weber 综合征(KTWS)。这是一种罕见的先天性疾病,其特征是火焰状痣、静脉和淋巴管畸形以及受累肢体的肥大。下肢最常受累。评估 KTWS 的常规方式有超声、CT、MRI、淋巴闪烁显像和血管造影。关于 KTWS 患者上肢的多模态影像学检查报告很少,这是首例 KTWS 红外热成像报告。